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Successful management of critical neonatal Ebstein’s anomaly with circular shunt

Published online by Cambridge University Press:  24 July 2025

Shota Masaki Open the ORCID record for Shota Masaki [Opens in a new window] ,
Yohji Nomura  and
Hiroomi Murayama
Shota Masaki*
Affiliation:
Department of Cardiovascular Surgery, Aichi Children’s Health and Medical Center, Obu, Aichi, Japan
Yohji Nomura
Affiliation:
Department of Pediatric Cardiology, Aichi Children’s Health and Medical Center, Obu, Aichi, Japan
Hiroomi Murayama
Affiliation:
Department of Cardiovascular Surgery, Aichi Children’s Health and Medical Center, Obu, Aichi, Japan
*
Corresponding author: Shota Masaki; Email: s.masaki6@outlook.jp
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Abstract

The prognosis of neonatal Ebstein’s anomaly requiring early surgery is poor, especially with a circular shunt. We report a critically ill case managed with emergency two-stage Starnes surgery immediately after birth. We hypothesised that the three components of the Starnes procedure, right ventricle exclusion, atrial septal defect creation, and systemic-to-pulmonary shunt, could be organised and reconstructed in a consecutive two-stage strategy to control postoperative circulatory fluctuations.

Keywords

Ebstein’s anomalyStarnes procedurecircular shunt

Information

Type
Case Report
Information
Cardiology in the Young , First View , pp. 1 - 3
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Copyright
© The Author(s), 2025. Published by Cambridge University Press

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References

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