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Progressive decline of arterial oxygen saturation measured by pulse oximetry in the patient with inferior vena cava obstruction: delayed impact of inherited haemoglobinopathy

Published online by Cambridge University Press:  06 August 2025

Yu Matsuo ,
Akira Sato  and
Hirofumi Saiki Open the ORCID record for Hirofumi Saiki [Opens in a new window]
Yu Matsuo
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Iwate Medical University, Shiwa, Japan
Akira Sato
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Iwate Medical University, Shiwa, Japan
Hirofumi Saiki*
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Iwate Medical University, Shiwa, Japan
*
Corresponding author: Hirofumi Saiki; Email: hirosaiki-circ@umin.ac.jp
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Abstract

Although inherited haemoglobinopathies may indicate low oxygen saturation measured by pulse oximetry (SpO2), the timing and mode of its decline after birth are unclear. Here, we present a patient with haemoglobin Köln disease who developed unexpected decline in SpO2 more than two years after heart surgery. Due to simultaneous identification of inferior vena cava stenosis, the differential diagnosis became complicated.

Keywords

Oxygen saturationhaemoglobincyanosisCHD

Information

Type
Brief Report
Information
Cardiology in the Young , First View , pp. 1 - 3
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Copyright
© The Author(s), 2025. Published by Cambridge University Press

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Footnotes

Drs. Yu Matsuo and Akira Sato are contributed equally to this work.

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