Hostname: page-component-65b85459fc-997vn Total loading time: 0 Render date: 2025-10-15T22:34:17.291Z Has data issue: false hasContentIssue false
  • English
  • Français

Anomalous origin of right pulmonary artery: diagnosis, treatment, and follow-up in an adult patient

Published online by Cambridge University Press:  06 July 2020

Susan Pumacayo-Cárdenas Open the ORCID record for Susan Pumacayo-Cárdenas [Opens in a new window] ,
Moises Jimenez-Santos  and
Edgar Quea-Pinto
Susan Pumacayo-Cárdenas*
Affiliation:
Departamento de Tomografía cardiaca, Instituto nacional de cardiología Ignacio Chávez, Ciudad de México, México
Moises Jimenez-Santos
Affiliation:
Departamento de Tomografía cardiaca, Instituto nacional de cardiología Ignacio Chávez, Ciudad de México, México
Edgar Quea-Pinto
Affiliation:
Departamento de cardiología intervencionista de cardiopatías congénitas, Instituto nacional de cardiología Ignacio Chávez, Ciudad de México, México
*
Author for correspondence: Susan Pumacayo-Cárdenas, Belisario Domínguez Sección 16, Belisario Domínguez Secc 16, Tlalpan, CDMX. Tel: +51979791469. E-mail: pumacayocardenas@gmail.com
Get access Rights & Permissions [Opens in a new window]

Abstract

Anomalous origin of a branch pulmonary artery from the aorta is a rare malformation, accounting for 0.12% of all congenital heart defects. We present the case of a 43-year-old man with an anomalous origin of the right pulmonary artery (AORPA) from the ascending aorta. Reimplantation of the right pulmonary artery was carried out successfully, with favourable evolution in the medium-term follow-up. It is the first described case that receives corrective treatment in adulthood with a favourable evolution.

Keywords

anomalous origin of one pulmonary arterycongenital heart diseasecomputed tomographycardiac catheterisation

Information

Type
Brief Report
Information
Cardiology in the Young , Volume 30 , Issue 8 , August 2020 , pp. 1199 - 1201
Copyright
© The Author(s), 2020. Published by Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

Article purchase

Temporarily unavailable

References

Wang, J, Song, Y, Cheng, TO, et al.The value of transthoracic echocardiography in the diagnosis of anomalous origin of the right pulmonary artery from the ascending aorta: a single center experience from China. Int J Cardiol 2015; 184: 750–754.CrossRefGoogle Scholar
Shakibi, AG, Rastan, H, Nazarian, I, et al.Isolated unilateral absence of the pulmonary artery. Review of the world literature and guidelines for surgical repair. Jpn Heart J 1978; 19: 439–451.CrossRefGoogle ScholarPubMed
Liu, H, Juan, YH, Chen, J, et al.Anomalous origin of one pulmonary artery branch from the aorta: role of MDCT angiography. AJR 2015; 204: 979–987.CrossRefGoogle ScholarPubMed
Prifti, E, Crucean, A, Bonacchi, M, et al. Postoperative outcome in patients with anomalous origin of pulmonary artery branch from the aorta. Eur J Cardiothorac Surg 2003; 24: 21–27.CrossRefGoogle ScholarPubMed
Higeno, R, Inamura, N, Kayatani, F.Unilateral absence of the pulmonary artery: a report of two cases that presented different clinical courses. Cardiol Young 2015; 25: 1399–1402.CrossRefGoogle ScholarPubMed
Bockeria, LA, Makhachev, OA, Tkh, K, et al. Congenital isolated unilateral absence of pulmonary artery and variants of collateral blood supply of the ipsilateral lung. Interact Cardiov Thorac Surg 2011; 12: 509–510.CrossRefGoogle ScholarPubMed
Pankaj, G, Sachin, T, Shyam, S, et al.The anomalous origin of one pulmonary artery branch from the aorta. Interact Cardio Vasc Thorac Surg 2012; 15: 86–92.Google Scholar
Raymond, A, Pedretti, E, Privitera, G, et al.Neonatal diagnosis of isolated absence of the right pulmonary artery: a case report and review of the literature. Ital J Pediatr 2018; 44: 27.CrossRefGoogle ScholarPubMed
Van der Feen, DE, Bartelds, B, de Boer, RA, Berger, R.Assessment of reversibility in pulmonary arterial hypertension and congenital heart disease. HEART 2019; 105: 276–282.CrossRefGoogle ScholarPubMed
Galie, N, Humbert, M, Vachiery, JL, et al.ESC/ERS guidelines for the diagnosis and treatment of pulmonary hypertension. Eur Respir J 2015; 46: 903–975.Google ScholarPubMed
Apitz, C, Hansmann, G, Schranz, D.Hemodynamic assessment and acute pulmonary vasoreactivity testing in the evaluation of children with pulmonary vascular disease. Expert consensus statement on the diagnosis and treatment of paediatric pulmonary hypertension. The European Paediatric Pulmonary Vascular Disease Network, endorsed by ISHLT and DGPK. Heart 2016; 102 (Suppl 2): 23–29.Google Scholar
Xie, L, Gao, L, Wu, Q, et al.Anomalous origin of the right pulmonary artery from the ascending aorta: results of direct implantation surgical repair in 6 infants. J Cardiothorac Surg 2015; 10: 97.CrossRefGoogle ScholarPubMed
Garg, P, Talwar, S, Kothari, SS, Saxena, A, Juneja, R, Choudhary, SK, Airan, B. The anomalous origin of the branch pulmonary artery from the ascending aorta. Interact Cadiovasc Thorac Surg 2012; 15 (1): 86–92.. doi: 10.1093/icvts/ivs110.CrossRefGoogle ScholarPubMed