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Successful treat-and-repair strategy in a 5 year old with partial anomalous pulmonary venous connection, atrial septal defect, and severe pulmonary hypertension

Published online by Cambridge University Press:  19 August 2025

Ken Hayashi Open the ORCID record for Ken Hayashi [Opens in a new window] ,
Kumiyo Matsuo  and
Hisaaki Aoki
Ken Hayashi*
Affiliation:
Department of Cardiology, Osaka Women’s and Children’s Hospital, Izumi, Osaka, Japan
Kumiyo Matsuo
Affiliation:
Department of Cardiology, Osaka Women’s and Children’s Hospital, Izumi, Osaka, Japan
Hisaaki Aoki
Affiliation:
Department of Cardiology, Osaka Women’s and Children’s Hospital, Izumi, Osaka, Japan
*
Corresponding Author: Ken Hayashi; Email: hayaken0103@hotmail.co.jp
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Abstract

We report the case of a 5-year-old boy with severe pulmonary arterial hypertension due to partial anomalous pulmonary venous connection and atrial septal defect. Sequential combination therapy using multiple pulmonary vasodilators enabled safe surgical repair. In this case of severe pulmonary arterial hypertension—associated with partial anomalous pulmonary venous connection and atrial septal defect—the treat-and-repair strategy proved effective.

Keywords

Partial anomalous pulmonary venous connectionpulmonary arterial hypertensiontreat-and-repairatrial septal defect

Information

Type
Case Report
Information
Cardiology in the Young , Volume 35 , Issue 8 , August 2025 , pp. 1727 - 1729
Copyright
© The Author(s), 2025. Published by Cambridge University Press

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References

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