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Lymphangiomatosis: a differential diagnosis of lytic lesions of the temporal bone

Published online by Cambridge University Press:  08 March 2017

M B Naguib ,
N Al-Jazan  and
T Hashem
M B Naguib*
Affiliation:
Department of Otolaryngology, King Faisal University, Al-Khobar, Saudi Arabia
N Al-Jazan
Affiliation:
Department of Otolaryngology, King Faisal University, Al-Khobar, Saudi Arabia
T Hashem
Affiliation:
Department of Pathology, King Faisal University, Al-Khobar, Saudi Arabia
*
Address for correspondence: Dr Maged B Naguib, POB 40008, Al-Khobar 31952, Kingdom of Saudi Arabia. E-mail: magedbaher@yahoo.com
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Abstract

Objective:

We report a histologically proved case of lymphangiomatosis of the skull, involving the temporal bone and presenting as multiple lytic bone lesions.

Method:

A case report and a review of the literature concerning lymphangiomatosis are presented.

Results:

Lymphangiomatosis affecting bones is a rare disorder caused by a congenital malformation of the lymphatic system, resulting in diffuse proliferation of the lymphatic channels and involving bones, parenchymal organs and soft tissue. Involved bones show massive osteolysis and progressive, localised bone resorption.

Conclusion:

Lymphangiomatosis should be kept in mind in the differential diagnosis of lytic lesions of the skull.

Keywords

LymphangiomatosisSkullTemporal Bone

Information

Type
Online Only Clinical Record
Information
The Journal of Laryngology & Otology , Volume 122 , Issue 11 , November 2008 , e23
Copyright
Copyright © JLO (1984) Limited 2008

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References

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