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The first reported treatment of Nager syndrome associated hearing loss with bone-anchored hearing aids: case report

Published online by Cambridge University Press:  12 October 2011

G P Davies  and
I J M Johnson
G P Davies*
Affiliation:
Newcastle University Medical School, Newcastle upon Tyne, UK
I J M Johnson
Affiliation:
BAHA Programme, Freeman Hospital, Newcastle upon Tyne, UK
*
Address for correspondence: Dr Gareth Peter Davies, Tudor Lodge, Brookfield Road, Churchdown, Gloucester GL3 2PF, UK Fax: +44 (0)1452 617 135 E-mail: g.p.davies1@ncl.ac.uk
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Abstract

Objective:

To report the first case of treatment of Nager syndrome associated conductive hearing loss with bone-anchored hearing aids, in a three-year-old boy.

Method:

Clinical case report and current literature review regarding the use of bone-anchored hearing aids in the treatment of conductive hearing loss in children.

Results:

A three year eight month old boy with Nager syndrome was successfully treated for conductive hearing loss using bilateral bone-anchored hearing aids.

Conclusion:

This is the first case report of the use of bone-anchored hearing aids to treat Nager syndrome associated conductive hearing loss. Treatment was safe and successful in this case.

Keywords

Acrofacial Dysostosis, Nager TypeBone-Anchored Hearing AidHearing Loss, Conductive

Information

Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 126 , Issue 1 , January 2012 , pp. 76 - 78
Copyright
Copyright © JLO (1984) Limited 2011

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References

1Herrmann, BW, Karzon, R, Molter, DW. Otologic and audiologic features of Nager acrofacial dysostosis. Int J Pediatr Otorhinolaryngol 2005;69:1053–9Google Scholar
2Opitz, C, Stoll, C, Ring, P. Nager, syndrome. Problems and possibilities of therapy. J Orofac Orthop 2000;61:226–36Google Scholar
3Zhang, Y, Dai, Y, Liu, Y, Ren, J. Mandibulofacial dysostosis, microtia, and limb anomalies in a newborn: a new form of acrofacial dysostosis syndrome? Clin Genet 2010;78:570–4Google Scholar
4Genetics Home Reference. In: http://ghr.nlm.nih.gov/condition/nager-syndrome [7 September 2011]Google Scholar
5Powell, RH, Burrell, SP, Cooper, HR, Proops, DW. The Birmingham bone anchored hearing aid programme: paediatric experience and results. J Laryngol Otol 1996;21(suppl):21–9Google Scholar
6Peyton's place. In: http://peytonsparents.blogspot.com [4 March 2011]Google Scholar
7The BAHAUsers Support Forum – Parental Chat. http://www.baha-users-support.com/cgi-bin/2bb/2bb.cgi?seq=msg&board=12&msg=1247846844&rn=6 [4 March 2011]Google Scholar
8Snik, A, Leijendeckers, J, Hol, M, Mylanus, E, Cremers, C. The bone-anchored hearing aid for children: recent developments. Int J Audiol 2008;47:554–9CrossRefGoogle ScholarPubMed
9Lloyd, S, Almeyda, J, Sirimanna, KS, Albert, DM, Bailey, CM. Updated surgical experience with bone-anchored hearing aids in children. J Laryngol Otol 2007;121:826–31CrossRefGoogle ScholarPubMed