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Vascular aneurysm producing divided right atrium in a patient with pulmonary atresia and intact ventricular septum

Published online by Cambridge University Press:  19 August 2008

John C. Wood ,
Miguel Reyes-Mugica  and
Gary Kopf
John C. Wood*
Affiliation:
Children's Heart Center, Division of Cardiology, Children's Hospital of Los Angeles, USC School of Medicine, Los Angeles, CAUSA
Miguel Reyes-Mugica
Affiliation:
Department of Pathology, Yale University School of Medicine, New Haven, ConnecticutUSA
Gary Kopf
Affiliation:
Department of Cardiothoracic Surgery, Yale University School of Medicine, New Haven, Connecticut, USA
*
Dr. John Wood, Childrens Heart center, Division of Cardiology, Childrens Hospital of Los Angeles, Mail Stop 34, Los Angeles, CA 90027, USA Tel: (323) 669–5470; Fax: (203) 669–7317; E-mail: jwood@usc.edu
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Abstract

We describe a patient with pulmonary atresia and intact ventricular septum in whom the right atrium was divided by a vascular aneurysm located in the right atrioventricular groove. We postulate that the structure represents an aneursymally dilated right coronary artery taking anomalous origin from the pulmonary trunk, with fistulous communication to the right atrium. We discuss the findings relative to concepts of development of the coronary arteries in normal hearts and in pulmonary atresia with an intact ventricular septum.

Keywords

Pulmonary atresiadivided tight atriumcor triatriatum dextercoronary arterial fistulaaneurysmanomalous coronary artery

Information

Type
Brief Reports
Information
Cardiology in the Young , Volume 10 , Issue 3 , May 2000 , pp. 281 - 285
Copyright
Copyright © Cambridge University Press 2000

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