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Unilateral absence of the pulmonary artery in a paediatric cohort

Published online by Cambridge University Press:  03 October 2025

Laia Brunet-Garcia Open the ORCID record for Laia Brunet-Garcia [Opens in a new window] ,
Flavio Zuccarino  and
Juan Manuel Carretero Bellon
Laia Brunet-Garcia
Affiliation:
Department of Paediatric cardiology, Consorci Sanitari del Maresme, Hospital de Mataró, Barcelona, Spain
Flavio Zuccarino
Affiliation:
Department of Radiology, Hospital Sant Joan de Déu, Barcelona, Spain Department of Radiology, Hospital del Mar, Barcelona, Spain
Juan Manuel Carretero Bellon*
Affiliation:
Department of Paediatric cardiology, Hospital Sant Joan de Déu, Barcelona, Spain Department of Paediatric cardiology, Hospital Universitari Joan XXIII, Universitat Rovira i Virgili, Tarragona, Spain
*
Corresponding author: Juan Manuel Carretero Bellon; Email: juan.carretero@sjd.es
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Abstract

We present six paediatric patients with unilateral absence of the pulmonary artery in pursuance of rising the clinician’s recognition. Unilateral absence of the pulmonary artery was misdiagnosed in one patient by echocardiography. One patient had corrective surgery of a complete atrioventricular septal defect, and another had a right lobectomy. The remaining patients did not undergo any intervention and were asymptomatic at the end of the study period. Although there is a lack of consensus regarding optimal surgical approach, we opted for a more conservative strategy with good results.

Keywords

Unilateral absence of pulmonary arterypulmonary artery abnormalitiesCHD

Information

Type
Case Report
Information
Cardiology in the Young , First View , pp. 1 - 3
Copyright
© The Author(s), 2025. Published by Cambridge University Press

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References

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