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The unconventional surgical management of an infant with rare Scimitar syndrome variant

Published online by Cambridge University Press:  07 October 2025

Thushara Rodrigo Open the ORCID record for Thushara Rodrigo [Opens in a new window] ,
Christopher Hilton Open the ORCID record for Christopher Hilton [Opens in a new window]  and
Graham Derrick
Thushara Rodrigo*
Affiliation:
Paediatric Cardiology, Great Ormond Street Hospital for Children NHS Trust, London, UK
Christopher Hilton
Affiliation:
Paediatric Cardiology, Great Ormond Street Hospital for Children NHS Trust, London, UK
Graham Derrick
Affiliation:
Paediatric Cardiology, Great Ormond Street Hospital for Children NHS Trust, London, UK
*
Corresponding author: Thushara Rodrigo; Email: thushara.rodrigo@gosh.nhs.uk
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Abstract

Scimitar syndrome is characterised by anomalous right pulmonary venous drainage to the inferior vena cava associated with right pulmonary artery hypoplasia. We present a case of an infant with Scimitar syndrome with a well-formed right pulmonary artery, in high Qp heart failure who was managed with right pulmonary artery banding after thorough haemodynamic evaluation.

Keywords

Scimitarheart failurepulmonary artery band

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Type
Case Report
Information
Cardiology in the Young , First View , pp. 1 - 3
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Copyright
© The Author(s), 2025. Published by Cambridge University Press

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