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Transcatheter correction of the scimitar variant with dual pulmonary venous drainage—an international multicentre series

Published online by Cambridge University Press:  10 October 2025

Tomohito Kogure Open the ORCID record for Tomohito Kogure [Opens in a new window] ,
Matthew I. Jones ,
Sebastian Goreczny ,
Iñaki Navarro-Castellanos ,
Mounir Riahi ,
Joaquim Miro  and
Shakeel A. Qureshi
Tomohito Kogure
Affiliation:
Department of Paediatric and Congenital Cardiology, Evelina London Children’s Hospital, London, UK Department of Cardiology, Tokyo Women’s Medical University, Tokyo, Japan
Matthew I. Jones
Affiliation:
Department of Paediatric and Congenital Cardiology, Evelina London Children’s Hospital, London, UK
Sebastian Goreczny
Affiliation:
Department of Paediatric and Cardiology, Jagiellonian University Medical College, Kraków, Poland
Iñaki Navarro-Castellanos
Affiliation:
Department of Paediatric Cardiology, Centre Hospitalier Universitaire Sainte-Justine, Montréal, Canada Department of Paediatric Cardiology, Children’s Hospital of Mexico Federico Gómez, Mexico City, Mexico
Mounir Riahi
Affiliation:
Department of Congenital Cardiology, Centre Hospitalier de l’Université de Montréal, Montréal, Canada
Joaquim Miro
Affiliation:
Department of Paediatric Cardiology, Centre Hospitalier Universitaire Sainte-Justine, Montréal, Canada
Shakeel A. Qureshi*
Affiliation:
Department of Paediatric and Congenital Cardiology, Evelina London Children’s Hospital, London, UK
*
Corresponding author: Shakeel A. Qureshi; Email: shakeel.qureshi1@nhs.net
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Abstract

Background:

Scimitar syndrome is an uncommon congenital malformation of pulmonary venous drainage to the junction of the right atrium and inferior caval vein. Treatment is usually surgical, depending on the morphological variant. When there is dual drainage of the anomalous veins to the inferior caval vein and the left atrium, a transcatheter procedure may represent an alternative to surgery.

Methods:

We report a series of four patients with the scimitar variant with dual pulmonary venous drainage treated with a transcatheter approach.

Result:

All four patients (three children, one adult) had dual drainage of right pulmonary veins into the inferior caval vein and to the left atrium via a connecting vein. All patients underwent a successful catheter occlusion of the anomalous connection to the systemic vein without complication. Vascular plug devices were used in two patients: a left atrial appendage closure device in one patient and a ventricular septal defect closure device in one patient. All the procedures resulted in complete occlusion of the anomalous venous drainage to the inferior caval vein and unobstructed drainage to the left atrium.

Keywords

Scimitar syndromepartial anomalous pulmonary venous connectiondual drainagetranscatheter correctionleft atrial appendage occluder

Information

Type
Original Article
Information
Cardiology in the Young , First View , pp. 1 - 4
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Copyright
© The Author(s), 2025. Published by Cambridge University Press

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