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Off-pump direct hepatic veins-to-hemiazygos vein anastomosis after primary Kawashima operation: long-term result

Part of: Surgery Functionally Univentricular Heart

Published online by Cambridge University Press:  08 March 2021

Renate Kaulitz Open the ORCID record for Renate Kaulitz [Opens in a new window] ,
Gerhard Ziemer  and
Michael Hofbeck Open the ORCID record for Michael Hofbeck [Opens in a new window]
Renate Kaulitz*
Affiliation:
Department of Pediatric Cardiology and Pediatric Intensive Care Medicine, Tuebingen University Children’s Hospital, Tuebingen, Germany
Gerhard Ziemer
Affiliation:
Pediatric Cardiac Surgery, Adult Congenital Heart Surgery, Geisinger Medical Center Heart Institute, Danville, PA, USA
Michael Hofbeck
Affiliation:
Department of Pediatric Cardiology and Pediatric Intensive Care Medicine, Tuebingen University Children’s Hospital, Tuebingen, Germany
*
Author for correspondence: Renate Kaulitz, MD, Department of Pediatric Cardiology and Pediatric Intensive Care Medicine, Tuebingen University Children’s Hospital, Hoppe-Seyler Str. 1 D-72076 Tuebingen, Germany. Tel: +49 7071 2984711; Fax: +49 7071 295693. E-mail: renate.kaulitz@med.uni-tuebingen.de
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Abstract

Direct hepatic veins-to-hemiazygos connection offers the balanced distribution of hepatic venous blood to both lungs, not requiring anticoagulation. We report a 13-year follow-up after this type of off-pump Fontan completion. Patient’s hepatic veins-to-hemiazygos confluence increased with growth to allow for unobstructed flow. This unique technique can be recommended in heterotaxy patients, if atrial hepatic venous drainage and hemiazygos vein are in close proximity.

Keywords

Kawashima operationheterotaxyleft isomerism

Information

Type
Brief Report
Information
Cardiology in the Young , Volume 31 , Issue 8 , August 2021 , pp. 1340 - 1342
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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