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Infracardiac total anomalous pulmonary venous drainage with concomitant hypoplastic aortic arch in a preterm neonate: a rare and complex surgical challenge

Published online by Cambridge University Press:  10 July 2025

Munavvar Gasimova Open the ORCID record for Munavvar Gasimova [Opens in a new window] ,
Bahruz Aliyev ,
Aynur Abbasaliyeva ,
Cabir Gulmaliyev ,
Khayala Mammadova  and
Shiraslan Bakhshaliyev Open the ORCID record for Shiraslan Bakhshaliyev [Opens in a new window]
Munavvar Gasimova*
Affiliation:
Anesthesiology and Intensive care, Liv Bona adea, Baku, Azerbaijan
Bahruz Aliyev
Affiliation:
Pediatric Cardiac Surgery Department, Liv Bona Dea Hospital, Baku, Azerbaijan
Aynur Abbasaliyeva
Affiliation:
Anesthesiology and Intensive care, Liv Bona adea, Baku, Azerbaijan
Cabir Gulmaliyev
Affiliation:
Cardiovascular surgery, Liv Bona Dea, Baku, Azerbaijan
Khayala Mammadova
Affiliation:
Pediatric Cardiac Surgery Department, Liv Bona Dea Hospital, Baku, Azerbaijan
Shiraslan Bakhshaliyev
Affiliation:
Pediatric Cardiac Surgery Department, Liv Bona Dea Hospital, Baku, Azerbaijan
*
Corresponding author: Munavvar Gasimova; E-mail: munavvar.gasimova1990@gmail.com
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Abstract

Total anomalous pulmonary venous drainage associated with hypoplastic aortic arch represents an exceptionally rare and intricate congenital cardiac anomaly. We report the case of a 13-day-old late preterm neonate presenting with infracardiac total anomalous pulmonary venous drainage, severe pulmonary hypertension, and a hypoplastic aortic arch. The patient underwent single-stage surgical correction involving rerouting of the pulmonary venous confluence to the left atrium and aortic arch reconstruction using autologous pericardial patch under cardiopulmonary bypass with selective cerebral perfusion. Postoperative recovery was favourable, marked by successful extubation, resolution of pulmonary hypertension, and absence of residual anatomical obstruction. This case highlights the feasibility and effectiveness of early, comprehensive surgical repair and the necessity of coordinated multidisciplinary perioperative care. Long-term follow-up remains vital for monitoring functional outcomes and detecting late complications.

Keywords

Total anomalous pulmonary venous drainagehypoplastic aortic archneonaterare case

Information

Type
Case Report
Information
Cardiology in the Young , Volume 35 , Issue 9 , September 2025 , pp. 1944 - 1946
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Copyright
© The Author(s), 2025. Published by Cambridge University Press

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